Diagnosis and treatment of cardiac amyloidosis: an interdisciplinary consensus statement

Summary The prevalence and significance of cardiac amyloidosis have been considerably underestimated in the past; however, the number of patients diagnosed with cardiac amyloidosis has increased significantly recently due to growing awareness of the disease, improved diagnostic capabilities and demo...

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Published in:Wiener Klinische Wochenschrift 2020-12, Vol.132 (23-24), p.742-761
Main Authors: Bonderman, Diana, Pölzl, Gerhard, Ablasser, Klemens, Agis, Hermine, Aschauer, Stefan, Auer-Grumbach, Michaela, Binder, Christina, Dörler, Jakob, Duca, Franz, Ebner, Christian, Hacker, Marcus, Kain, Renate, Kammerlander, Andreas, Koschutnik, Matthias, Kroiss, Alexander Stephan, Mayr, Agnes, Nitsche, Christian, Rainer, Peter P., Reiter-Malmqvist, Susanne, Schneider, Matthias, Schwarz, Roland, Verheyen, Nicolas, Weber, Thomas, Zaruba, Marc Michael, Badr Eslam, Roza, Hülsmann, Martin, Mascherbauer, Julia
Format: Article
Language:English
Subjects:
Amyloid Neuropathies, Familial
Cardiomyopathies - diagnosis
Cardiomyopathies - therapy
Consensus
Consensus Report
Endocrinology
Gastroenterology
Humans
Internal Medicine
Medicine
Medicine & Public Health
Pneumology/Respiratory System
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Summary:Summary The prevalence and significance of cardiac amyloidosis have been considerably underestimated in the past; however, the number of patients diagnosed with cardiac amyloidosis has increased significantly recently due to growing awareness of the disease, improved diagnostic capabilities and demographic trends. Specific therapies that improve patient prognosis have become available for certain types of cardiac amyloidosis. Thus, the earliest possible referral of patients with suspicion of cardiac amyloidosis to an experienced center is crucial to ensure rapid diagnosis, early initiation of treatment, and structured patient care. This requires intensive collaboration across several disciplines, and between resident physicians and specialized centers. The aim of this consensus statement is to provide guidance for the rapid and efficient diagnosis and treatment of light-chain amyloidosis and transthyretin amyloidosis, which are the most common forms of cardiac amyloidosis.
ISSN:0043-5325
1613-7671
DOI:10.1007/s00508-020-01781-z