A Case of Adolescent Cronkhite-Canada Syndrome

The Cronkhite-Canada syndrome (CCS) was first reported in 1955, since then more than 500 cases have been reported, indicating an estimated incidence of one case per 1 million inhabitants. The syndrome occurs predominantly in male, with a ratio of three males to two females. Because of the rarity of...

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Bibliographic Details
Published in:Gastroenterology research 2018-02, Vol.11 (1), p.64-67
Main Authors: Faria, Mikaell Alexandre Gouvea, Basaglia, Bruna, Nogueira, Vinicius Quintiliano Moutinho, de Mendonca, Tatiana Barros Gama Ferraz, Kaiser Junior, Roberto Luiz, Filho, Idiberto Jose Zotarelli, de Quadros, Luiz Gustavo
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Language:English
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Case Report
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Summary:The Cronkhite-Canada syndrome (CCS) was first reported in 1955, since then more than 500 cases have been reported, indicating an estimated incidence of one case per 1 million inhabitants. The syndrome occurs predominantly in male, with a ratio of three males to two females. Because of the rarity of the syndrome, there are no evidence-based therapies and the treatments described include a combination of therapies, but none is consistently effective. Surgery is usually reserved for the treatment of complications. Herein, we present a case of adolescent CCS. The patient was a 15-year-old boy who presented with watery diarrhea with 20 episodes a day, vomiting and abdominal pain for 4 weeks, with a weight loss of 8.0 kg (15.0% of initial weight). Endoscopic examination revealed polyposis in the stomach, duodenum, and colon. CCS was diagnosed and the patient was treated with a combined corticosteroid and metronidazole. Followed up at 8 month after the diagnosis, the patient was asymptomatic.
ISSN:1918-2805
1918-2813
DOI:10.14740/gr912w