A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia

Primary cutaneous follicle centre lymphoma (PCFCL) is a rare cutaneous B cell lymphoma in middle-age adults with excellent prognosis. Here we present a case of a patient with a PCFCL in the form of a giant tumour of the scalp in combination with a myeloproliferative neoplasm, JAK2V617F positive esse...

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Bibliographic Details
Published in:Biomarker research 2014-04, Vol.2 (1), p.7-7, Article 7
Main Authors: Tirefort, Yordanka, Pham, Xuan-Cuong, Ibrahim, Yasmine Lucile, Lecompte, Thomas Pierre, Matthes, Thomas, Prins, Christa, Cortes, Begonia, Bernimoulin, Michael, Chalandon, Yves, Samii, Kaveh
Format: Article
Language:English
Subjects:
Care and treatment
Case Report
Case studies
Diagnosis
Non-Hodgkin's lymphomas
Prognosis
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Summary:Primary cutaneous follicle centre lymphoma (PCFCL) is a rare cutaneous B cell lymphoma in middle-age adults with excellent prognosis. Here we present a case of a patient with a PCFCL in the form of a giant tumour of the scalp in combination with a myeloproliferative neoplasm, JAK2V617F positive essential thrombocythaemia. This case may be of interest because of the favourable outcome in spite of the large size of the PCFCL, the rare combination with essential thrombocythaemia and because it contributes to discussion on the role of JAK2 mutation in such patients.
ISSN:2050-7771
2050-7771
DOI:10.1186/2050-7771-2-7