Keratosis follicularis spinulosa decalvans: case report

Keratosis follicularis spinulosa decalvans is a rare disease, with genetic transmission either X-linked or sporadic, characterized by follicular hyperkeratosis and cicatricial alopecia. The disease usually begins in early childhood exacerbating throughout adolescence. The therapies are somewhat effe...

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Bibliographic Details
Published in:Anais brasileiros de dermatología 2010-07, Vol.85 (4), p.537-540
Main Authors: Berbert, Alceu L C V, Mantese, Sônia A O, Rocha, Ademir, Cherin, Cláudia P, Couto, Carolina M
Format: Article
Language:eng ; por
Subjects:
Alopecia - etiology
Alopecia - pathology
Child, Preschool
Darier Disease - complications
Darier Disease - diagnosis
Darier Disease - pathology
Female
Humans
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Summary:Keratosis follicularis spinulosa decalvans is a rare disease, with genetic transmission either X-linked or sporadic, characterized by follicular hyperkeratosis and cicatricial alopecia. The disease usually begins in early childhood exacerbating throughout adolescence. The therapies are somewhat effective, with frustrating treatment when there are changes which are predominantly cicatricial. It is reported a case of child with intense cicatricial alopecia, with precocious changes (already present at birth) that rapidly evolved to diffuse cicatricial alopecia on the scalp, which has limited the treatment, with disappointing results.
ISSN:1806-4841
DOI:10.1590/s0365-05962010000400017