Cervical cord tethering due to split cord malformation at the cervico-dorsal junction presenting with self-mutilation of the fingers

An unusual case of cervical spinal cord tethering with diplomyelia is described. A 12-month old female presented with self-mutilation of the fingers due to sensory loss in the hands, absent reflexes, poor muscle tone, and reduced distal upper-limb movements. There was a deep skin dimple overlying th...

Full description

Saved in:
Bibliographic Details
Published in:Developmental medicine and child neurology 2002-12, Vol.44 (12), p.844-848
Main Authors: Myles, L M, Steers, A J W, Minns, R
Format: Article
Language:English
Subjects:
Case Reports
Congenital Impairments
Female
Fingers
Humans
Infant
Magnetic Resonance Imaging
Neural Tube Defects - etiology
Neural Tube Defects - surgery
Pregnancy
Reflex, Abnormal - physiology
Self-Injurious Behavior - diagnosis
Self-Injurious Behavior - psychology
Spinal Cord - abnormalities
Spinal Cord - surgery
Young Children
Citations: Items that cite this one
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:An unusual case of cervical spinal cord tethering with diplomyelia is described. A 12-month old female presented with self-mutilation of the fingers due to sensory loss in the hands, absent reflexes, poor muscle tone, and reduced distal upper-limb movements. There was a deep skin dimple overlying the T1 spinous process. Imaging showed angulation of the lower cervical cord and an operation revealed a low cervical meningocele and a split cord malformation with tethering of one half of the cord; the cord was untethered. In this report the literature is reviewed.
ISSN:0012-1622
1469-8749
DOI:10.1017/S0012162201003024