Primary malignant peripheral nerve sheath tumor of the lung in a young child without neurofibromatosis type 1

Malignant peripheral nerve sheath tumors (MPNST) are uncommon in children and almost half of the cases occur in patients with neurofibromatosis 1 (NF1). We report a child with a primary MPNST of the lung without NF1. MPNST of the lung has similar clinical and radiologic characteristics as pleuropulm...

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Bibliographic Details
Published in:Pediatric Blood & Cancer 2006-10, Vol.47 (5), p.636-638
Main Authors: Muwakkit, Samar A., Rodriguez-Galindo, Carlos, EL Samra, Ahmad I., Khoury, Ruby, Akel, Samir R., Mroueh, Salman, Razzouk, Bassem, Abboud, Miguel R.
Format: Article
Language:English
Subjects:
Biological and medical sciences
Child
Diagnosis, Differential
General aspects
Humans
lung
Lung Neoplasms - diagnosis
Lung Neoplasms - pathology
Lung Neoplasms - therapy
Magnetic Resonance Imaging - methods
Male
malignant peripheral nerve sheath tumor
Medical sciences
Neoplasms, Multiple Primary - diagnosis
Neoplasms, Multiple Primary - pathology
Neoplasms, Multiple Primary - therapy
Nerve Sheath Neoplasms - diagnosis
Nerve Sheath Neoplasms - pathology
Nerve Sheath Neoplasms - therapy
Neurofibromatosis 1 - diagnosis
Predictive Value of Tests
Pulmonary Blastoma - diagnosis
Pulmonary Blastoma - pathology
Pulmonary Blastoma - therapy
Tomography, X-Ray Computed - methods
Tumors
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Description
Summary:Malignant peripheral nerve sheath tumors (MPNST) are uncommon in children and almost half of the cases occur in patients with neurofibromatosis 1 (NF1). We report a child with a primary MPNST of the lung without NF1. MPNST of the lung has similar clinical and radiologic characteristics as pleuropulmonary blastoma. We suggest to include MPNST of the lung in the differential diagnosis of intrapulmonary masses in children. Pediatr Blood Cancer 2006; 47:636–638. © 2006 Wiley‐Liss, Inc.
ISSN:1545-5009
1545-5017
1096-911X
DOI:10.1002/pbc.20787