The re-occurrence of dilated cardiomyopathy in propionic acidemia after liver transplantation requiring heart transplant, first case from Middle East

Propionic acidemia is a rare autosomal recessive inborn error of metabolism. It is relatively common in Middle East. Dilated cardiomyopathy is one of the leading causes of morbidity and mortality for patients with propionic acidemia. Liver transplantation has been used for patient with frequent meta...

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Bibliographic Details
Published in:	Cardiology in the young 2023-01, Vol.33 (1), p.86-89
Main Authors:	Hejazi, Yahia, Hijazi, Ziyad M., Al-saloos, Hesham, Omran, Tawfeg Ben
Format:	Article
Language:	eng
Subjects:	Acidosis Age Amino acids Cardiac function Cardiology Cardiomyopathy COVID-19 Dilated cardiomyopathy Ejection fraction Enzymes General Cardiology Genes Heart failure Heart transplantation Heart transplants Inborn errors of metabolism Infections Liver Liver transplantation Liver transplants Medical screening Metabolism Morbidity Myocarditis Original Article Ostomy Patient admissions Pediatrics Plasma Propionic acidemia Transplantation
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Summary:	Propionic acidemia is a rare autosomal recessive inborn error of metabolism. It is relatively common in Middle East. Dilated cardiomyopathy is one of the leading causes of morbidity and mortality for patients with propionic acidemia. Liver transplantation has been used for patient with frequent metabolic decompensations and was shown to be beneficial in propionic acidemia-related dilated cardiomyopathy. Up to our knowledge, there has been one reported case of recurrent dilated cardiomyopathy 3 years after liver transplantation. We report the first case, from Middle East, of recurrent dilated cardiomyopathy, 6 years after liver transplantation.
ISSN:	1047-9511 1467-1107