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Multimodality treatment including whole pleura radiation therapy for DICER1‐associated pediatric pleuropulmonary blastoma
Limited data are available regarding radiation therapy in pediatric pleuropulmonary blastoma (PPB). We report the case of a 3‐year‐old girl with type II PPB successfully treated with trimodality therapy including multiagent chemotherapy, resection, and whole pleura radiation therapy. While longer fo...
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Published in: | Pediatric blood & cancer 2021-06, Vol.68 (6), p.e29004-n/a |
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Main Authors: | , , , , , , |
Format: | Article |
Language: | English |
Subjects: | |
Citations: | Items that this one cites Items that cite this one |
Online Access: | Get full text |
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Summary: | Limited data are available regarding radiation therapy in pediatric pleuropulmonary blastoma (PPB). We report the case of a 3‐year‐old girl with type II PPB successfully treated with trimodality therapy including multiagent chemotherapy, resection, and whole pleura radiation therapy. While longer follow‐up is required to confirm ultimate local tumor control and long‐term post‐treatment sequelae, currently 3.5 years following therapy, she is well, without recurrent disease or observable toxicity. The goal of this report is to add our experience to the literature regarding PPB, its management, and treatment, as prospective randomized controlled trials are not feasible due to the rarity of this disease. |
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ISSN: | 1545-5009 1545-5017 |
DOI: | 10.1002/pbc.29004 |