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Hereditary haemorrhagic telangiectasia manifesting as subdural empyema

Hereditary haemorrhagic telangiectasia (HHT) also known as Osler-Weber-Rendu disease is a rare autosomal dominant condition causing vascular dysplasia. Cerebral abscess formation, secondary to paradoxical septic emboli via HHT-derived pulmonary arteriovenous malformations (pAVMs) in this context is...

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Published in:British journal of neurosurgery 2016-06, Vol.30 (3), p.356-358
Main Authors: Solanki, Sandeep P, Taylor, Christopher, Robertson, Iain
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Robertson, Iain
description Hereditary haemorrhagic telangiectasia (HHT) also known as Osler-Weber-Rendu disease is a rare autosomal dominant condition causing vascular dysplasia. Cerebral abscess formation, secondary to paradoxical septic emboli via HHT-derived pulmonary arteriovenous malformations (pAVMs) in this context is well documented. Herein, we present the first case of subdural empyema with this aetiology.
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subjects Arteriovenous Fistula - diagnosis
Arteriovenous Fistula - surgery
Arteriovenous Malformations - diagnosis
Arteriovenous Malformations - surgery
Brain Abscess - complications
Brain Abscess - diagnosis
Brain Abscess - surgery
Empyema, Subdural - diagnosis
Empyema, Subdural - surgery
Female
Genetic disorders
Humans
Middle Aged
Neurosurgery
Pulmonary Artery - abnormalities
Pulmonary Artery - surgery
Pulmonary Veins - abnormalities
Pulmonary Veins - surgery
Telangiectasia, Hereditary Hemorrhagic - diagnosis
Telangiectasia, Hereditary Hemorrhagic - surgery
title Hereditary haemorrhagic telangiectasia manifesting as subdural empyema
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