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Hereditary haemorrhagic telangiectasia manifesting as subdural empyema

Hereditary haemorrhagic telangiectasia (HHT) also known as Osler-Weber-Rendu disease is a rare autosomal dominant condition causing vascular dysplasia. Cerebral abscess formation, secondary to paradoxical septic emboli via HHT-derived pulmonary arteriovenous malformations (pAVMs) in this context is...

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Bibliographic Details
Published in:British journal of neurosurgery 2016-06, Vol.30 (3), p.356-358
Main Authors: Solanki, Sandeep P, Taylor, Christopher, Robertson, Iain
Format: Article
Language:English
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Summary:Hereditary haemorrhagic telangiectasia (HHT) also known as Osler-Weber-Rendu disease is a rare autosomal dominant condition causing vascular dysplasia. Cerebral abscess formation, secondary to paradoxical septic emboli via HHT-derived pulmonary arteriovenous malformations (pAVMs) in this context is well documented. Herein, we present the first case of subdural empyema with this aetiology.
ISSN:0268-8697
1360-046X
DOI:10.3109/02688697.2016.1155695