Glomuvenous malformation: magnetic resonance imaging findings

We report a case of a glomuvenous malformation involving the dorsal aspect of the right hand and distal forearm in an 11-year-old boy. He had a history of multiple vascular anomalies since birth and presented with increasing right hand pain. MRI played an important role in characterizing and determi...

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Bibliographic Details
Published in:Pediatric radiology 2015-02, Vol.45 (2), p.286-290
Main Authors: Flors, Lucia, Norton, Patrick T., Hagspiel, Klaus D.
Format: Article
Language:English
Subjects:
Case Report
Child
Contrast Media
Diagnosis, Differential
Forearm - blood supply
Glomus Tumor - diagnosis
Glomus Tumor - pathology
Glomus Tumor - surgery
Hand - blood supply
Humans
Imaging
Magnetic Resonance Imaging - methods
Male
Medicine
Medicine & Public Health
Neuroradiology
Nuclear Medicine
Oncology
Pediatrics
Radiology
Ultrasound
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Description
Summary:We report a case of a glomuvenous malformation involving the dorsal aspect of the right hand and distal forearm in an 11-year-old boy. He had a history of multiple vascular anomalies since birth and presented with increasing right hand pain. MRI played an important role in characterizing and determining the extent of the lesion. In particular, dynamic time-resolved contrast-enhanced MR angiography precisely defined its vascularity. The diagnosis was made histopathologically after partial resection of the lesion. Glomuvenous malformation is a rare developmental hamartoma that originates from the glomus body. Clinically they usually resemble a venous malformation but they are a different entity. In the appropriate clinical setting this rare condition must be included in the differential diagnosis of a vascular malformation, especially when subtle arterial enhancement, early venous shunting and progressive filling of dilated venous spaces are depicted on MRA.
ISSN:0301-0449
1432-1998
DOI:10.1007/s00247-014-3086-x