Autopsy-proven Acute Hemorrhagic Leukoencephalitis in an Elderly Patient

Acute Hemorrhagic Leukoencephalitis (AHLE), also known as Weston-Hurst syndrome, or Hurst's disease, is a hyperacute autoimmune demyelinating disease of the white matter, believed to be a severe variant of Acute Disseminated Encephalomyelitis (ADEM). It comprises 2% of cases of ADEM. Acute Hemo...

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Bibliographic Details
Published in:Canadian journal of neurological sciences 2014-01, Vol.41 (1), p.99-102
Main Authors: dos Santos, Marlise P., Martin, Jason, Woulfe, John, Lim, Siok P., Chakraborty, Santanu
Format: Article
Language:English
Subjects:
Aged
Autopsy
Brain - pathology
Brief Communications
Fatal Outcome
Humans
Leukoencephalitis, Acute Hemorrhagic - pathology
Male
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Summary:Acute Hemorrhagic Leukoencephalitis (AHLE), also known as Weston-Hurst syndrome, or Hurst's disease, is a hyperacute autoimmune demyelinating disease of the white matter, believed to be a severe variant of Acute Disseminated Encephalomyelitis (ADEM). It comprises 2% of cases of ADEM. Acute Hemorrhagic Leukoencephalitis is relatively rare, with less than 100 cases reported in the scientific literature3. We report an autopsy-proven case of AHLE with atypical clinical features and involving primarily the brainstem.
ISSN:0317-1671
2057-0155
DOI:10.1017/S031716710001636X