Magic syndrome and true aortic aneurysm

Magic syndrome is a very uncommon disease, and vascular involvement is exceptional; only one case has been reported in the literature associated to a true aortic aneurysm. The treatment of aneurysms recommended in these patients is based on isolated cases and includes corticosteroids, other immunosu...

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Bibliographic Details
Published in:Clinical rheumatology 2008-01, Vol.27 (1), p.115-117
Main Authors: Hidalgo-Tenorio, C., Sabio-Sánchez, J. M., Linares, P. J. P., Salmerón, L. M., Ros-Die, E., Jiménez-Alonso, J.
Format: Article
Language:English
Subjects:
Adult
Aneurysms
Aortic Aneurysm - complications
Aortic Aneurysm - pathology
Aortic Aneurysm - surgery
Behcet Syndrome - complications
Behcet Syndrome - pathology
Behcet Syndrome - therapy
Case Report
Cyclophosphamide - therapeutic use
Drug Therapy, Combination
Fatal Outcome
Female
Glucocorticoids - therapeutic use
Humans
Immunosuppressive Agents - therapeutic use
Medicine
Medicine & Public Health
Methylprednisolone - therapeutic use
Polychondritis, Relapsing - complications
Polychondritis, Relapsing - pathology
Polychondritis, Relapsing - therapy
Prednisone - therapeutic use
Rheumatology
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Description
Summary:Magic syndrome is a very uncommon disease, and vascular involvement is exceptional; only one case has been reported in the literature associated to a true aortic aneurysm. The treatment of aneurysms recommended in these patients is based on isolated cases and includes corticosteroids, other immunosuppressant drugs, and surgery. We report a case of a patient with Magic syndrome who developed aneurysm at the end of the aorta during treatment with infliximab, corticosteroids, and cyclosporine and who needed endovascular prosthesis implantation. After 12 months, she suffered an aneurysm of the ascending aorta, dilatation of the sinotubular junction, and severe aortic insufficiency, which forced surgery. During this time, the patient finally died.
ISSN:0770-3198
1434-9949
DOI:10.1007/s10067-007-0688-9