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Ivacaftor Reverses Airway Mucus Abnormalities in a Rat Model Harboring a Humanized G551D-CFTR
by
Birket, Susan E
,
Davis, Joy M
,
Fernandez-Petty, Courtney M
,
Henderson, Alexander G
,
Oden, Ashley M
,
Tang, LiPing
,
Wen, Hui
,
Hong, Jeong
,
Fu, Lianwu
,
Chambers, Andre
,
Fields, Alvin
,
Zhao, Gojun
,
Tearney, Guillermo J
,
Sorscher, Eric J
,
Rowe, Steven M
Published in
American journal of respiratory and critical care medicine
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American Journal Of Respiratory And Critical Care Medicine
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Airway Management
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Aminophenols - Therapeutic Use
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Animals
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Chloride Channel Agonists - Therapeutic Use
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Critical Care Medicine
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Cystic Fibrosis
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Cystic Fibrosis - Drug Therapy
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Cystic Fibrosis - Genetics
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Cystic Fibrosis Transmembrane Conductance Regulator - Drug Effects
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Cystic Fibrosis Transmembrane Conductance Regulator - Genetics
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G551D
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General & Internal Medicine
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Humans
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Ivacaftor
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Life Sciences & Biomedicine
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Lung Diseases
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Mucus
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Mucus - Drug Effects
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