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Degradation of Stop Codon Read-through Mutant Proteins via the Ubiquitin-Proteasome System Causes Hereditary Disorders
by
Shibata, Norihito
,
Ohoka, Nobumichi
,
Sugaki, Yusuke
,
Onodera, Chiaki
,
Inoue, Mizuho
,
Sakuraba, Yoshiyuki
,
Takakura, Daisuke
,
Hashii, Noritaka
,
Kawasaki, Nana
,
Gondo, Yoichi
,
Naito, Mikihiko
Published in
The Journal of biological chemistry
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Journal Of Biological Chemistry
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Journal Of Biological Chemistry/The Journal Of Biological Chemistry
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The Journal Of Biological Chemistry
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Animals
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Apoptosis
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Casp8 And Fadd-Like Apoptosis Regulating Protein - Genetics
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Casp8 And Fadd-Like Apoptosis Regulating Protein - Metabolism
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Cflip-L
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Codon, Terminator
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Genetic Diseases, Inborn - Genetics
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Homozygote
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Hsd3B2
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Mice
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Mice, Mutant Strains
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Molecular Bases Of Disease
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Mutagenesis
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Mutation
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Pnpo
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Proteasome
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Proteasome Endopeptidase Complex - Metabolism
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Protein Binding
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Read-Through Mutation
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Ribonucleoproteins - Metabolism
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